| CASE REPORT |
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| Year : 2018 | Volume
: 7
| Issue : 3 | Page : 181-184 |
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Prune-Belly syndrome with VACTERL association: A rare case
Sudhir Singh1, Jiledar Rawat1, Nitin Pant1, Sarita Singh2
1 Department of Paediatric Surgery, King George's Medical University, Lucknow, Uttar Pradesh, India
2 Department of Anesthesia, King George's Medical University, Lucknow, Uttar Pradesh, India
Correspondence Address:
Dr. Sudhir Singh
Department of Paediatric Surgery, King George's Medical University, Lucknow - 226 003, Uttar Pradesh
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/jcn.JCN_25_18
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Prune-Belly syndrome (PBS) is a rare congenital anomaly. It consists of genital and urinary abnormalities with partial or complete absence of abdominal wall musculature. Intrauterine consequences of this syndrome are oligohydramnios, pulmonary hypoplasia, and Potter's facies. Occasionally, the syndrome can have a broad spectrum of affected anatomy with different levels of severity. Here, we are reporting a rare case of PBS with VACTERL association. Six cases have been reported till now in English literature.
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