CASE REPORT |
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Year : 2016 | Volume
: 5
| Issue : 1 | Page : 58-60 |
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Kasabach Merritt syndrome: Is there a role of surgery?
Priya Dhruv Dhandore, Narendra Narayan Hombalkar, Chandrakant Kamlesh Pancholi
Department of General Surgery, Government Medical College Miraj and P. V. P. Government Hospital, Sangli, Maharashtra, India
Correspondence Address:
Chandrakant Kamlesh Pancholi Ex-surgery resident, Department of General Surgery, Government Medical College Miraj and P. V. P. Government Hospital, Sangli, Maharashtra India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/2249-4847.173280
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Kasabach–Merritt syndrome (KMS) is a rare clinical presentation in patients with preexisting hemangioma. Abnormal trapping of platelets within proliferating blood vessels and subsequent premature activation of coagulation cascades lead to thrombocytopenia and coagulopathy. Management of KMS is often challenging particularly in neonates without any fixed protocols for treatment. Management strategies include use of corticosteroids, propranolol, compression, embolization, use of interferon, laser therapy, sclerotherapy, chemotherapy, radiation, and/or surgery. The treatment plan should be individualized depending on type of vascular anomalies, age at presentation and patient response. We hereby present a rare case of KMS in a neonate with giant congenital hemangioma successfully managed surgically at our institute. |
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