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 Table of Contents  
IMAGES IN CLINICAL NEONATOLOGY
Year : 2012  |  Volume : 1  |  Issue : 3  |  Page : 166-167

Ectopia cordis


1 Department of Paediatrics, Tata Motors Hospital, Jamshedpur, India
2 BCCL Hospital, Dhanbad, Jharkhand, India

Date of Web Publication28-Sep-2012

Correspondence Address:
Rajiv Sharan
Tata Motors Hospital, Jamshedpur, Jharkhand
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/2249-4847.101708

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  Abstract 

Ectopia cordis is a rare congenital anomaly. Congenital anomaly scan can detect it at 18-23 weeks of gestation. Four chamber view of the heart in routine fetal anomaly scans at >18 weeks is the most effective technique to detect CHD prenatally.

Keywords: Ectopia cordis, cardiac anomaly, fetal anomaly scan


How to cite this article:
Amitabh P, Sharan R, Talapatra A. Ectopia cordis. J Clin Neonatol 2012;1:166-7

How to cite this URL:
Amitabh P, Sharan R, Talapatra A. Ectopia cordis. J Clin Neonatol [serial online] 2012 [cited 2020 Jul 13];1:166-7. Available from: http://www.jcnonweb.com/text.asp?2012/1/3/166/101708


  Introduction Top


Ectopia cordis: This case is that of a 1-day-old female born at 34 weeks of gestation by Emergency LSCS [Figure 1]. Baby had normal APGAR and examination revealed chest wall defect with mediastinal contents outside. Antenatal USG did reveal a pulsating mass outside the body cavity, but it was overlooked [Figure 2]. Antenatal fetal anomaly scan at 18-24 weeks can diagnose 50% of the major congenital heart disease. However routine four-chamber view appears to be inadequate for the outflow tract lesions, and therefore specific assessment of the outflow tracts is necessary to improve the detection rate.
Figure 1: Ectopia cordis

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Figure 2: Fetal anomaly scan – ectopia cordis

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Postnatal ECHO and CT thorax revealed AV canal defect with pulmonary hypoplasia.


  Discussion Top


Ectopia cordis is a rare anomaly with a prevalence of 0.08/10,000 live births. [1] Four types have been recognized, viz., (1) thoracic (65%), (2) thoraco-abdominal (20%), (3) abdominal (10%), and (4) cervical. [2],[3]

It is associated with other congenital defects, e.g. hydrocephalus, cleft palate, congenital heart defects, hypoplastic lung disease, skeletal dysplasia, diaphragmatic hernia, abdominal wall defect, etc. [4]

Management

Prognosis is poor and parents should be counseled for mid-trimester termination of pregnancy. Attempts at surgical correction have been largely unsuccessful.

 
  References Top

1.Khoury MJ. Ectopiacordis, midline defects and chromosome abnormalities: An epidemiologic perspective. Am J Med Genet 1988;30:811-7.  Back to cited text no. 1
    
2.Blatt ML. Ectopiacordis: Report of a case and review of the literature. Am J Dis Child 1942;63:515.  Back to cited text no. 2
    
3.Byron F. Ectopiacordis: Report of a case with attempted operative correction. J Thorac Surg 1949;17:717-22.  Back to cited text no. 3
    
4.Cantrell JR. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium, and heart. Surg Gynecol Obstet 1958;107:602-14.  Back to cited text no. 4
    


    Figures

  [Figure 1], [Figure 2]


This article has been cited by
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Joseph Merola,Geoffrey Adrian Tipper,Zakier Hussain,Venkataraman Balakrishnan,Peter Gan
British Journal of Neurosurgery. 2014; : 1
[Pubmed] | [DOI]



 

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